Expresión de búsqueda: MALIGNANT ATROPHIC PAPULOSIS 
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Descriptor Inglés:   Malignant Atrophic Papulosis 
Descriptor Español:   Papulosis Atrófica Maligna 
Descriptor Portugués:   Papulose Atrófica Maligna 
Sinónimos Inglés:   Degos Disease
Kohlmeier-Degos Disease  
Categoría:   C14.907.137.520
C14.907.940.530
C17.800.862.457
Definición Inglés:   Variously described as a vasculopathy, endovasculitis, or occlusive arteriopathy, this condition occurs in a benign cutaneous form and a lethal multiorgan systemic variant. It is characterized by a narrowing and occlusion of the lumen of small to medium-sized blood vessels, leading to ischemia and infarction in the involved organ systems. The etiology and pathophysiology are unknown. 
Nota de Indización Inglés:   malignant does not refer to neoplasm; do not confuse with the neoplasm ACANTHOMA, DEGOS see ACANTHOMA
Nota Histórica Inglés:   2008 
Calificadores Permitidos Inglés:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications CN congenital
DI diagnosis DH diet therapy
DT drug therapy EC economics
EM embryology EN enzymology
EP epidemiology EH ethnology
ET etiology GE genetics
HI history IM immunology
ME metabolism MI microbiology
MO mortality NU nursing
PS parasitology PA pathology
PP physiopathology PC prevention & control
PX psychology RA radiography
RI radionuclide imaging RT radiotherapy
RH rehabilitation SU surgery
TH therapy US ultrasonography
UR urine VE veterinary
VI virology  
Número del Registro:   52617 
Identificador Único:   D054853 

Ocurrencia en la BVS:
 

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